Lhermitte-Duclos disease: A case report and literature review.
10.11817/j.issn.1672-7347.2021.190574
- Author:
Zhiqiang LIU
1
;
Yanqing HE
2
;
Jiaxin FU
3
;
Jun WU
2
;
Tao SONG
2
;
Ying WANG
2
;
Tianxiang HUANG
4
Author Information
1. Department of Neurosurgery, Xiangya Hospital, Central South University, Changsha 410008. zhiqiangliu668@163.com.
2. Department of Neurosurgery, Xiangya Hospital, Central South University, Changsha 410008.
3. Grade of 2015 in Oral Medicine, Medical College of Jinzhou Medical University, Jinzhou Liaoning 121001, China.
4. Department of Neurosurgery, Xiangya Hospital, Central South University, Changsha 410008. 2567244544@qq.com.
- Publication Type:Review
- Keywords:
Lhermitte-Duclos disease;
diagnosis;
treatment
- MeSH:
Cerebellar Neoplasms/surgery*;
Cerebellum;
Hamartoma Syndrome, Multiple/diagnostic imaging*;
Humans;
Magnetic Resonance Imaging;
Neoplasm Recurrence, Local
- From:
Journal of Central South University(Medical Sciences)
2021;46(2):195-199
- CountryChina
- Language:English
-
Abstract:
Lhermitte-Duclos disease (LDD) is a type of rare brain tumor located in posterior fossa. A patient with LDD located in the left cerebellum and vermis was admitted by the Department of Neurosurgery, Xiangya Hospital, Central South University. MRI scan showed slightly heterogeneous enhancement at the region close to vermis. The patient underwent partial resection on August 11, 2016 without postoperative chemoradiotherapy. The progress free survival was 11 months and the overall survival was 17 months. What the case reveals is that the partial resection is not beneficial to these patients with LDD as the residual lesion probably recurs in a short term after operation. The pathogenesis, diagnosis and treatment of LDD are explored and summarized in combination with relevant literature.