Rhabdomyosarcoma of the common bile duct mimicking choledochal cyst: a rare cause of obstructive jaundice.
- Author:
Hassan NAZMUL
1
;
Islam RAFIQUL
1
;
Fathema KANIZ
1
;
Sayeed MAIMUNA
1
;
Wahiduzzaman Mazumder MD
1
;
Bazlul Karim ASM
1
;
Pada Dey BISHNU
2
Author Information
1. Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh.
2. Department of Pathology, Faculty of Basic Science and Paraclinical Science, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh.
- Publication Type:Journal Article
- MeSH:
Child;
Choledochal Cyst;
Common Bile Duct/pathology*;
Diagnosis, Differential;
Humans;
Jaundice, Obstructive/etiology*;
Male;
Rhabdomyosarcoma, Embryonal/diagnosis*
- From:
Chinese Journal of Contemporary Pediatrics
2020;22(12):1338-1343
- CountryChina
- Language:Chinese
-
Abstract:
Extrahepatic biliary tract tumors are rare and among them rhabdomyosarcoma is most common. Rhabdomyosarcoma is a soft tissue malignant musculoskeletal tumor and is a very rare malignancy of the common bile duct in children. It usually presents as obstructive jaundice and/or pruritus. If there is no local invasion to the adjacent tissues, the radiological appearance of the tumor lesion is like a choledochal cyst. So the diagnosis is usually made at surgery or by preoperative biopsy. It is important to diagnose early and differentiate it from choledochal cyst and start treatment as early as possible for long time survival of the patient. This case report presented a case of a 10-year-old boy with recurrent onset of obstructive jaundice and fever preoperatively who was diagnosed as choledochal cyst and postoperatively as embryonal rhabdomyosarcoma of the common bile duct. After surgical resection and postoperative chemotherapy, the child had a good prognosis. So it is crucial to know that this rare tumor can mimic congenital choledochal cyst and it should be considered in the differential diagnosis of obstructive jaundice in children.
