Sequential Hybrid Repair of Aorta and Bilateral Common Iliac Arteries Secondary to Chronic Aortic Dissection with Extensive Aneurysmal Degeneration in a Marfan Patient.
10.5758/vsi.2017.33.3.112
- Author:
Carlos A HINOJOSA
1
;
Javier E ANAYA-AYALA
;
Hugo LAPARRA-ESCARENO
;
Rene LIZOLA
;
Adriana TORRES-MACHORRO
Author Information
1. Department of Surgery, Section of Vascular Surgery and Endovascular Therapy, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico. carlos.a.hinojosa@gmail.com
- Publication Type:Case Report
- Keywords:
Marfan syndrome;
Chronic aortic dissection;
Aneurysmal degeneration;
Hybrid repair
- MeSH:
Adult;
Aneurysm*;
Angiography;
Aorta*;
Aortic Aneurysm, Thoracic;
Aortic Diseases;
Chest Pain;
Connective Tissue;
Female;
Follow-Up Studies;
Humans;
Iliac Artery*;
Marfan Syndrome;
Mortality;
Polyethylene Terephthalates;
Rupture;
Transplants
- From:Vascular Specialist International
2017;33(3):112-116
- CountryRepublic of Korea
- Language:English
-
Abstract:
Marfan syndrome is a connective tissue disorder associated with aortic dissection, aneurysmal degeneration and rupture. These cardiovascular complications represent the main cause of mortality, therefore repair is indicated. We present a 35-year-old woman who experienced acute onset of chest pain. Her imaging revealed a chronic DeBakey type I dissection with aortic root dilation and descending thoracic aneurysmal degeneration. She underwent a Bentall procedure and endovascular exclusion of the descending thoracic aortic aneurysm. She was closely followed and 2 years later a computed tomography angiography (CTA) revealed the aneurysmal degeneration of the thoracoabominal aorta and bilateral iliac arteries. The patient underwent a composite reconstruction using multi-visceral branched and bifurcated Dacron grafts. At 5 years from her last surgery, a CTA revealed no new dissection or further aneurysmal degenerations. Aortic disease in Marfan patients is a complex clinical problem that may lead to secondary or tertiary aortic reconstructions; close follow-up is mandatory.
