Contralateral Single Lung Re-transplantation in the Patient with Lymphangioleiomyomatosis due to Graft Failure.
- Author:
Eun Kyu JOUNG
1
;
Hyo Chae PAIK
;
Jung Joo HWANG
;
Jae Ho KIM
;
Young Nam YOUN
;
Doo Yun LEE
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Yongdong Severance Hospital, Yonsei University College of Medicine, Korea. hcpaik@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Lung transplantation;
Reoperation;
Lymphangioleiomyomatosis
- MeSH:
Adult;
Female;
Follow-Up Studies;
Humans;
Lung Transplantation;
Lung*;
Lymphangioleiomyomatosis*;
Pneumonectomy;
Rare Diseases;
Recurrence;
Reoperation;
Respiratory Insufficiency;
Tracheostomy;
Transplants*;
Ventilators, Mechanical
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2006;39(4):323-327
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Lymphangioleiomyomatosis (LAM) is a rare disease in women of childbearing ages that eventually leads to respiratory failure. Lung transplantation is the only conclusive therapeutic modality in end-stage LAM. While single-lung transplantation is the preferred operation, the graft failure or recurrence of LAM was reported. We performed a single lung transplantation on a 36-year-old woman suffering from respiratory failure due to lymphangioleiomyomatosis. After a 1-year follow up, the patient was readmitted because of graft failure with collapsed transplanted lung. The lung volume reduction surgery (LVRS), tracheostomy and ventilator care were performed. However, neither the medical nor surgical treatment had any effect. Subsequently, we performed a contralateral single lung re-transplantation and had a good postoperative results.
