Surgical ligation of porto-systemic shunt for the treatment of type Ⅱ Abernethy malformation in 12 children
10.3760/cma.j.cn113855-20200510-00374
- VernacularTitle:外科结扎门体分流治疗12例Ⅱ型Abernethy畸形的疗效分析
- Author:
Jinshan ZHANG
1
;
Xinghai CHEN
;
Long LI
;
Wenying HOU
Author Information
1. 首都儿科研究所普外科,北京 100020
- From:
Chinese Journal of General Surgery
2020;35(10):792-796
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To investigate the feasibility and effectiveness of surgical ligation in the treatment of congenital extra-hepatic portosystemic shunt (Abernethy malformation) in children.Methods:Among the 12 children with Abernethy malformation admitted at our hospital, 9 cases for blood stools, 2 cases for elevated transaminase level and jaundice, and 1 case for hypoxemia. Intraoperatively, if portal pressure was ≤ 26 cm H 2O(1 cmH 2O=0.098 kPa) after clamping the shunt, than the shunt was ligated, when>26 cm H 2O, the portosystemic shunt was partially ligated and the shunt was completely ligated in a two stage. All patients were followed up for 5-70 months (mean: 35.2 months). Results:Six cases underwent the one stage ligation of portosystemic shunt, five cases underwent the two stage ligation and one case with partial ligation of portosystemic shunt. The symptoms of hematochezia relieved in 9 cases. The levels of blood bilirubin and transaminase returned to normal after operation in 2 cases with increased transaminase. The oxygen saturation returned to normal in 1 case with hypoxemia.Conclusion:The surgical ligation of portosystemic shunt is an effective method to treat type Ⅱ Abernethy malformation.