The value of echocardiography in the diagnosis of persistent fifth aortic arch and its classification
10.3760/cma.j.cn131148-20200522-00420
- VernacularTitle:永存第五主动脉弓的超声心动图诊断价值及其分型探讨
- Author:
Lin ZHENG
1
;
Fangyun WANG
;
Xin ZHANG
;
Yongli CAO
;
Qun WU
;
Guiqin MA
;
Yan SUN
;
Jingya LI
;
Pei LI
;
Ning MA
Author Information
1. 国家儿童医学中心 首都医科大学附属北京儿童医院心脏超声科 100045
- From:
Chinese Journal of Ultrasonography
2020;29(10):857-863
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To study the classification of persistent fifth aortic arch (PFAA) and the value of echocardiography in the diagnosis of PFAA.Methods:A total of 16 cases (male 6, female 10, at ages from 7 days to 4 years and 2 months old, the median age was 3 months) diagnosed with PFAA in Beijing Children′s Hospital Affiliated to Capital Medical University from January 2013 to June 2019 were studied retrospectively. The diagnosis standard, differential methods and misdiagnosed analysis of different subtypes of PFAA by echocardiography were summarized and analyzed.Results:The 16 cases included 1 case of type A1 double lumen aortic arch, 8 cases of type A2 single-lumen aortic arch, 3 cases of type B1 with pulmonary atresia and 4 cases of type B3 pulmonary artery branch arising from the distal end of ascending aorta. Only one patient of double lumen aortic arch missed diagnosis by echocardiography, and the rest were accurately diagnosed by echocardiography. CTA was performed in 13 cases, including 9 cases of type A, 1 case of type B1 and 3 cases of type B3, which confirmed the echocardiography diagnosis. Seven cases of Type A2 were operated.Conclusions:PFAA is a rare and complicated aortic arch malformation, which is divided into four major classification and multiple subtypes. Echocardiography can diagnose the PFAA and its classification, it is of great clinical significance for the early diagnosis, treatment and prognosis of children.