Research progress on congenital heart diseases of diminutive pulmonary blood
10.3760/cma.j.cn101070-20191111-01118
- VernacularTitle:肺血减少型先天性心脏病研究进展
- Author:
Hongyu CHEN
1
;
Tiewei LYU
Author Information
1. 重庆医科大学附属儿童医院心血管内科,儿童发育疾病研究教育部重点实验室,国家儿童健康与疾病临床医学研究中心,儿童发育重大疾病国家国际科技合作基地,儿科学重庆市重点实验室 400014
- From:
Chinese Journal of Applied Clinical Pediatrics
2020;35(13):1031-1034
- CountryChina
- Language:Chinese
-
Abstract:
Congenital heart diseases of diminutive pulmonary blood are characterized by the decrease of pulmonary blood flow accompanied with pulmonary stenosis or atresia.Diminutive pulmonary blood leads to abnormal development of lung, the formation of major aorta pulmonary collateral arteries (MAPCAs) and a complex cardiac anatomy structure in children, thereby resulting in serious clinical symptoms, poor quality of life and even life-threatening conditions.Therefore, diminutive pulmonary blood is a thorny problem in the treatment of cardiac malformation.However, the etiology and pathogenesis of this disease have not been elucidated yet.The clinical treatment plan and time depend on the disease type and MAPCAs.In this paper, the etiology, pathogenesis, diagnosis and treatment progress of congenital heart diseases of diminutive pulmonary blood were reviewed.