Two Cases of Primary Sclerosing Cholangitis.
- Author:
Chang Hong LEE
;
Jae Seon KIM
;
Young Tae BAK
;
Jin Ho KIM
;
Jong Guk KIM
;
Kwan Soo BYUN
;
Jong Eun YEON
;
Kyoung Min KIM
;
Ie Byung PARK
- Publication Type:Case Report
- Keywords:
Primary sclerosing cholangitis
- MeSH:
Bile Ducts;
Cholangiography;
Cholangitis, Sclerosing*;
Cicatrix;
Diagnosis;
Inflammation;
Liver Cirrhosis, Biliary;
Liver Failure;
Natural History
- From:Korean Journal of Gastrointestinal Endoscopy
1995;15(4):788-795
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Prirnary sclerosing cholangitis, a chronic progressive cholestatic hepatobiliary disorder of unknown etiology, is characterized by inflammation, scarring and obliteration of bile duct leading to biliary cirrhosis and liver failure. Because histologic finding has only a limited role in the diagnosis, the gold standard for establishing the diagnosis is cholangiographic demonstration of typical diffuse biliary stricutre or beading. The natural history is extremely variable. We report two cases of primary sclerosing cholangitis diagnosed by repeated endoscopic retrograde cholangiographies. They were followed up for 7 and 2 years, respectively.