A case of dyke-davidoff-masson syndrome associated with hypopituitarism and diabetes mellitus.
- Author:
So Yeon PARK
1
;
Mi Young LEE
;
Jae Hyun KIM
;
Song Yi KIM
;
Jang Yel SHIN
;
Young Goo SHIN
;
Choon Hee CHUNG
Author Information
1. Department of Internal Medicine, Yonsei University Wonju College of Medicine, Wonju, Korea. cchung@yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Dyke-Davidoff-Masson syndrome;
Hypopituitarism;
Diabetes mellitus
- MeSH:
Adult;
Amides;
Atrophy;
Diabetes Mellitus;
Facial Asymmetry;
Glucose Tolerance Test;
Hemiplegia;
Humans;
Hyperglycemia;
Hypertrophy;
Hypopituitarism;
Intellectual Disability;
Mastoid;
Paranasal Sinuses;
Paresis;
Polydipsia;
Polyuria;
Seizures;
Sulfones
- From:Korean Journal of Medicine
2010;79(3):316-320
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dyke-Davidoff-Masson syndrome (DDMS) is a rare condition characterized by asymmetric cerebral hemispheric growth with unilateral atrophy, ipsilateral compensatory osseous hypertrophy, hyperpneumatization of the paranasal sinuses and mastoid cells, and contralateral paresis. Varying degrees of hemiparesis, hemiplegia, seizures, mental retardation, and facial asymmetry can be associated with DDMS. We report the case of a 26-year-old man with DDMS associated with hypopituitarism who complained of polydipsia and polyuria. After an oral glucose tolerance test, he was diagnosed with type 2 diabetes. There is no report of DDMS associated with other pituitary dysfunction or hyperglycemia. Clinicians should consider the possibility of coexisting pituitary dysfunction or type 2 diabetes in patients with DDMS, as it is obviously important for the patient's outcome.
