Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia.
10.4070/kcj.2008.38.10.514
- Author:
Yongkeun CHO
1
Author Information
1. Department of Internal Medicine, School of Medicine, Kyungpook National University, Daegu, Korea. choyk@mail.knu.ac.kr
- Publication Type:Review
- Keywords:
Cardiomyopathies;
Arrhythmia;
Right ventricle
- MeSH:
Arrhythmias, Cardiac;
Cardiomyopathies;
Death, Sudden;
Electrocardiography;
Heart Failure;
Heart Ventricles;
Humans;
Myocardium;
Syncope
- From:Korean Circulation Journal
2008;38(10):514-523
- CountryRepublic of Korea
- Language:English
-
Abstract:
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by rogressive, fibrofatty replacement of the myocardium, ventricular arrhythmia, sudden death, and progressive heart failure. ARVC/D may be an important cause of syncope, ventricular arrhythmias, electrocardiogram (ECG) abnormalities and/or non-ischemic wall motion abnormalities. Some patients, however, do not have a typical clinical presentation. Thus, a high clinical suspicion and extensive studies may be needed to establish the diagnosis of ARVC/D. Recent progress in diagnostic modalities and a better understanding of the clinical manifestations of ARVC/D may lead to optimal management of affected patients.
