A Case of Benign Intracranial Hypertension in Pseudopseudohypoparathyroidism.
- Author:
Won Young JUNG
1
;
Sang Jin KANG
;
Hak Yeon BAE
Author Information
1. Department of Neurology, Chosun University Medical College, Kwangju, Korea.
- Publication Type:Case Report
- Keywords:
Pseudopseudohypoparathyroidism;
Benign intracranial hypertension;
Albright's hereditary osteodystrophy
- MeSH:
Abducens Nerve Diseases;
Adolescent;
Brain;
Calcium;
Craniocerebral Trauma;
Diplopia;
Headache;
Humans;
Magnetic Resonance Imaging;
Male;
Metacarpal Bones;
Neurologic Examination;
Papilledema;
Parathyroid Hormone;
Phosphorus;
Pseudopseudohypoparathyroidism*;
Pseudotumor Cerebri*;
Vomiting
- From:Journal of the Korean Neurological Association
1999;17(3):431-434
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We describe a rare case of pseudopseudohypoparathyroidism (PPHP) with benign intracranial hypertension (BIH). A 16 year-old male presented with headache, vomiting, ocular pain, blurred vision, and diplopia following minor head trauma. He showed developmental delay, short stature and short metacarpals and phalanges, which suggested Albright's hereditary osteodystrophy. Neurologic examination revealed bilateral sixth cranial nerve palsy and bilateral papilledema. Lumbar puncure disclosed an elevated opening CSF pressure with normal biochemical and celluar find-ings. However, the levels of serum calcium, phosphorus and parathyroid hormone were within the normal limits and chromosomal analyses were normal. Brain MRI revealed normal ventricular size and no structural abnormality. We concluded that PPHP seemed to have a key role for the genesis of BIH in this case, although previous mild head trauma might have a precipitating effect.
