Otologic Evaluation in Children with Turner Syndrome.
- Author:
Jung Soo KIM
1
;
Sang Ryul KIM
;
Woo Yeong CHUNG
Author Information
1. Department of Pediatrics, College of Medicine, Inje University, Busan Paik Hospital, Busan, Korea. chungwy@chollian.net
- Publication Type:Original Article
- Keywords:
Turner syndrome;
Hearing loss;
Otitis media
- MeSH:
Child*;
Ear;
Hearing;
Hearing Loss;
Hearing Loss, Bilateral;
Hearing Loss, Unilateral;
Humans;
Incidence;
Karyotype;
Otitis Media;
Quality of Life;
Turner Syndrome*
- From:Journal of Korean Society of Pediatric Endocrinology
2005;10(1):71-75
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: Patients with Turner syndrome have been frequently suspected to have associated various otologic disorders and hearing loss. The purpose of this study was to evaluate the otologic problems in children with Turner Syndrome. METHODS: Twenty patients aged 5 to 20 years who were diagnosed as Turner syndrome were evaluated audiologically. RESULTS: Five subjects (25.0%) had previous histories of otitis media. An audiological examination was performed for all subjects and revealed normal hearing in 13 patients (65.0%), unilateral hearing loss in 3 patients (15.0%) and bilateral hearing loss in 4 patients (20.0%). Type of the hearing loss was conductive in 3 ears (7.5%), mixed in 2 ears (5.0%) and sensorineural in 6 ears (15.0%). Degree of hearing loss was mild in 9 ears, moderate in 1 ear and moderately severe in 1 ear. The incidence of hearing loss according to the karyotype revealed 10 ears (41.7%) in total deletion of Xp but only 1 ear (6.3%) in partial deletion of Xp. CONCLUSION: Our results demonstrated that the otitis media and hearing loss were one of the common findings in children with Turner syndrome. These results emphasize the importance of regular otological examinations and audiological evaluation in children with Turner syndrome for quality of life.
