Surgical Treatment of Primary Pulmonary Artery Sarcoma
- VernacularTitle:肺動脈原発肉腫に対して外科的治療を施行した1例
- Author:
Masayuki NISHIYAMA
1
;
Hiroaki SASAKI
1
;
Kouki YOKAWA
1
;
Takayuki SHIJYO
1
;
Yosuke INOUE
1
;
Yoshimasa SEIKE
1
;
Kyokun UEHARA
1
;
Hitoshi MATSUDA
1
Author Information
- Keywords: pulmonary hypertension; primary pulmonary artery sarcoma
- From:Japanese Journal of Cardiovascular Surgery 2020;49(6):366-369
- CountryJapan
- Language:Japanese
- Abstract: We present a 62-year-old woman who was diagnosed with primary pulmonary arterial sarcoma with pulmonary hypertension. CT showed a large defect inside both main pulmonary arteries in accordance with the accumulation of FDG-PET. To relieve the symptom and to prevent sudden death, removal of a massive pulmonary tumor and postoperative chemotherapy were planned. Utilizing the intermittent systemic circulatory arrest under deep hypothermia (18°C), the pulmonary artery trunk and both main pulmonary arteries were opened. The tumor stacking inside the pulmonary artery was removed and its origin at the commissure of the pulmonary artery valve was resected. The defect was repaired with a pulmonary valve replacement. Histopathological examination revealed high grade sarcoma. Her postoperative course was uneventful ; however, she died of cerebral hemorrhage during chemotherapy six months after surgery.
