Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin
- Author:
Young Hun CHUNG
1
;
Jin Woo JANG
;
Jae Young CHO
Author Information
- Publication Type:Case Report
- From:Archives of Plastic Surgery 2020;47(1):92-96
- CountryRepublic of Korea
- Abstract: Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma originating from the sheaths of peripheral nerves. Approximately 50% of MPNSTs occur in patients with neurofibromatosis (NF). These tumors often present as deep soft tissue lesions, arising from the nerve plexuses of the extremities or from the nerves extending from the trunk. They rarely occur in the skin, especially in patients with NF. Herein, we report our experience with an MPNST of the skin in a patient with NF.
