Fontan Conversion for Patients with Protein-Losing Enteropathy after a Björk Procedure with Patent Right Atrium to Innominate Vein Bypass
- VernacularTitle:右房・無名静脈バイパスが開存していた Glenn 手術原法・ Björk 手術後遠隔期の蛋白漏出性胃腸症に対し TCPC 転換術を施行した1例
- Author:
Shuichi SHIRAISHI
1
;
Ai SUGIMOTO
1
;
Masanori TSUCHIDA
1
Author Information
- Keywords: protein-losing enteropathy; TCPC conversion; Björk procedure
- From:Japanese Journal of Cardiovascular Surgery 2020;49(5):257-260
- CountryJapan
- Language:Japanese
- Abstract: A 37-year-old male patient who had previously undergone left original Blalock-Taussig shunt, original Glenn shunt, left pulmonary artery patch plasty, and a Björk procedure was referred to our hospital due to protein-losing enteropathy. Because he suffered from severe low-cardiac output syndrome immediately after the Björk procedure, mechanical circulatory support and construction of the bypass between the right atrial appendage and the innominate vein using an artificial graft were required. We performed a Fontan-revision operation : total cavopulmonary connection with extra-cardiac conduit, right atrial ablation, pacemaker lead implantation, construction of fenestration between the conduit and the atrium, and reconstruction of the left pulmonary artery in front of the ascending aorta successfully. His postoperative course was uneventful and protein-losing enteropathy had not recurred 3 years after the operation.
