A Case of Juvenile Xanthogranuloma Associated with Juvenile Chronic Myeloid Leukemia and Neurofibromatosis.
- Author:
Joo Young ROH
;
Hyang Joon PARK
;
Yong Woo CINN
;
Soo Nam KIM
;
Soon Gyum KIM
- Publication Type:Case Report
- Keywords:
Juvenile xanthogranuloma;
Juveile chronic myeloid leukemia;
Neurofibro - matosis
- MeSH:
Cafe-au-Lait Spots;
Child;
Humans;
Infant;
Leukemia, Myelogenous, Chronic, BCR-ABL Positive*;
Male;
Neurofibromatoses*;
Xanthogranuloma, Juvenile*
- From:Korean Journal of Dermatology
1987;25(3):404-409
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Juvenile xanthogranuloma(JXG) is a a benign histiocytic proliferative disorder most frequently seen in infants. The usual course is self-limited, but it may be a manifestation of juvenile chronic myeloid leukemia(JCML). In addition to JXG, some patient with JCML may have multiple cafe-au-lait spots and a family history of neurofibromatosis(NF). The association of JXG and cafe-au-lait spots in patients with JCML is of interest in light of description of otherwise healthy children with JXG who also had cafe-au-lait spots. We report herein a case of JXG in 18-month-old boy who also had multiple cafe-au-alit spots, which predated the JCML.
