Intracranial Rosai-Dorfman disease in a child: A case report and literature review.
10.11817/j.issn.1672-7347.2019.05.019
- Author:
Wenyang LI
1
;
Xiang ZHAO
1
;
Gelei XIAO
1
;
Jie ZHAO
1
;
Jingping LIU
1
Author Information
1. Department of Neurosurgery, Xiangya Hospital, Central South University, Changsha 410008, China.
- Publication Type:Case Reports
- MeSH:
Biopsy;
Child;
Histiocytosis, Sinus;
Humans;
Male;
Neurosurgical Procedures;
Postoperative Period
- From:
Journal of Central South University(Medical Sciences)
2019;44(5):600-604
- CountryChina
- Language:Chinese
-
Abstract:
Intracranial Rosai-Dorfman disease (RDD) is a rare clinical histiocytosis proliferative disease. A 12-year-old boy with dizziness and headache for 1 month was admitted into Pediatric Neurosurgery of Xiangya Hospital, Central South University. The patient underwent total tumor resection and postoperative application of hormones and chemotherapy. During follow-up of 8 months, patient's condition was stable and no tumor recurrence was observed. For patient with a trend of tumor progression, stereotactic biopsy can help to confirm the diagnosis and determine the surgical strategy such as disposal of bone flaps. The treatment is mainly based on surgical intervention, supplemented by radiotherapy, chemotherapy and hormone therapy. Without affecting the nerve function, the surgeon should try to completely resect the tumor.