Diagnostic criteria and treatment progress of PHACE syndrome
10.3760/cma.j.issn.1002-0098.2017.11.011
- VernacularTitle: PHACE综合征的诊断标准及治疗进展
- Author:
Longlong SUN
1
;
Bin SUN
1
;
Yuchun MA
1
;
Hongzhao LEI
1
;
Changxian DONG
1
Author Information
1. Department of Hemangioma Surgery, People's Hospital of Zhengzhou University, Zhengzhou 450003, China
- Publication Type:Review
- Keywords:
Hemangioma;
PHACE syndrome;
Diagnostic criteria;
Treatment
- From:
Chinese Journal of Stomatology
2017;52(11):700-703
- CountryChina
- Language:Chinese
-
Abstract:
PHACE syndrome is a syndrome of multiple organ and multisystem abnormalities associated with infantile segmental hemangioma, characterized by abnormal posterior fossa development, infant hemangioma, aortic abnormalities, aortic coarctation and heart defects, eye anomalies and other symptoms. The incidence of the disease is low, but there exist life-threatening factors. Once clinically diagnosed, it should be highly valued and multidisciplinary consultation must be conducted. This article reviews the diagnostic criteria of PHACE syndrome and its associated facial segmental hemangioma, as well as the treatment and prognosis of brain abnormalities.
