A Case of Persistent Mullerian Duct Syndrome.
- Author:
Woo Il KIM
1
;
Young Jun LEE
;
Jung Hang LEE
;
Sang Min YOON
;
Ju Hong KIM
;
Joon Mee KIM
Author Information
1. Department of Urology, Inha University, College of Medicine, Sungnam, Korea.
- Publication Type:Case Report
- Keywords:
Persistent mullerian duct syndrome
- MeSH:
46, XY Disorders of Sex Development;
Cryptorchidism;
Disorders of Sex Development;
Fallopian Tubes;
Female;
Hernia, Inguinal;
Humans;
Male;
Orchiopexy;
Sertoli Cells;
Uterus
- From:Korean Journal of Urology
1994;35(2):198-201
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Male pseudohermaphroditism can result from defects in androgen synthesis, androgen action, and mullerian duct regression, and from other uncertain causes. A rare form of male pseudo- hermaphroditism is characterized by the persistence of mullerian derivative in phenotypic male. The retention of mullerian structures can be ascribed to failure of the Sertoli cells to synthesize mullerian duct inhibitory factor, a defect in the response of the duct to that factor, or possibly discordant timing of the release of that factor. We experienced a case of persistent mullerian duct syndrome, which is phenotypically normal male with a right inguinal hernia and a left undescended testis, bilateral fallopian tubes and a uterus. Herein we report a case of early orchiopexy with this syndrome and brief review of the literatures.
