Clinical characteristics of bronchopulmonary foregut malformation
10.3760/cma.j.issn.0578-1310.2017.08.016
- VernacularTitle: 支气管肺前肠畸形临床特征分析
- Author:
Jun LIU
1
;
Ju YIN
;
Xiuyun LIU
;
Yinghui HU
;
Xiaoli MA
;
Rui ZHANG
;
Qi ZENG
;
Baoping XU
;
Kunling SHEN
Author Information
1. Department of Respiratory Medicine, Beijing Children′s Hospital Affiliated to Capital Medical University, China National Clinical Specialty of Pediatric Respiratory Medicine, China National Clinical Research Center for Respiratory Diseases, Beijing 100045, China
- Publication Type:Clinical Trail
- Keywords:
Bronchopulmonary sequestration;
Signs and symptoms;
Radiography;
Diagnosis
- From:
Chinese Journal of Pediatrics
2017;55(8):628-631
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To analyze the clinical characteristics, diagnosis and treatment of bronchopulmonary foregut malformation(BPFM).
Method:The clinical manifestations, imaging findings and treatment of 8 patients with BPFM were analyzed retrospectively from January 2006 to May 2016 in Beijing Children′s Hospital.
Result:The age of children varied from 2 months to 7 years and 3 children were male while 5 female. Symptoms showed cough in 6 cases, fever in 4 cases, bucking when intaking of fluids or foods in 3 cases, tachypnea in 1 case, wheezing in 1 case, vomiting in 1 case, haematemesis in 1 case Pulmonary signs were decreased breath sounds in 4 cases, phlegm rale in 3 cases, shortness of breath in 2 cases, wheeze in 1 case, and retraction in 1 case. The upper gastrointestinal series showed abnormal fistulous tracts arising from the esophagus or the gastric fundus and extending into the mass in the lung. CT showed pulmonary sequestration and prompted the tube between lung and esophagus. Six children underwent pneumonectomy and esophageal fistula repair. They were discharged and their symptoms were improved. Two cases of children were discharged from a hospital without surgery.
Conclusion:Bronchopulmonary foregut malformation usually has its onset in early stage of life. The most common symptoms include recurrent pneumonia or bucking when intaking of fluids or foods. CT can demonstrate the bronchopulmonary sequestration and evaluate the communication with the gastrointestinal tract. The upper gastrointestinal series can demonstrate the abnormal tract directly. Pneumonectomy and esophageal fistula repair are the treatment of this disease.
