Clinical characteristics, diagnosis and treatment of pulmonary inflammatory myofibroblastic tumor in children
10.3760/cma.j.issn.0253-3766.2017.04.013
- VernacularTitle: 小儿肺部炎性肌纤维母细胞瘤的临床特征及诊治方法
- Author:
Fenghua WANG
1
;
Jianhua LIANG
1
;
Jiahang ZENG
1
;
Jue TANG
1
;
Hui WANG
1
;
Wei LIU
1
Author Information
1. Department of Thoracic Surgery, Guangzhou Women and Children's Medical Central, Guangzhou 510120, China
- Publication Type:Clinical Trail
- Keywords:
Neoplasms, muscle tissue;
Lung neoplasms;
Child;
Diagnosis;
Treatment
- From:
Chinese Journal of Oncology
2017;39(4):299-302
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To explore the clinical characteristics, diagnosis and treatment of pulmonary inflammatory myofibroblastic tumor in children.
Methods:The clinical data of 13 patients with pulmonary inflammatory myofibroblastic tumor between October 2009 and October 2015 were retrospectively analyzed, including 9 boys and 4 girls aged 1 to 12 years 4 months (mean 4 years 9 months). Seven patients underwent total tumor resection, 4 had lobectomy, 1 had partial tumor resection and 1 had biopsy. The follow-up time ranged from 2 months to 6 years and 2 months.
Results:Among the 13 patients, 9 were cured. Two patients lived with tumor. One of them had tumor which shrinked gradually and the other had stable disease. One patient with multiple lesions encountered recurrence after 3 operations and developed suspicious hepatic metastasis. One died during the operation because of airway mismanagement.
Conclusions:Pulmonary inflammatory myofibroblastic tumor in children has rather good prognosis while a few cases have the potential of recurrence and canceration. Surgery is the primary therapeutic approach. Close post-operative follow up is necessary.
