Progress in managing pulmonary arterial hypertension associated with congenital heart disease
10.3760/cma.j.issn.2095-428X.2019.13.017
- VernacularTitle: 先天性心脏病相关肺动脉高压研究进展
- Author:
Zhuoyuan XU
1
;
Qiangqiang LI
;
Hong GU
Author Information
1. Beijing Anzhen Hospital, Capital Medical University, Beijing Institute of Heart, Lung and Blood Vessel Disease, Beijing 100029, China
- Publication Type:Review
- Keywords:
Congenital heart disease;
Pulmonary arterial hypertension;
Child
- From:
Chinese Journal of Applied Clinical Pediatrics
2019;34(13):1030-1032
- CountryChina
- Language:Chinese
-
Abstract:
Pulmonary arterial hypertension(PAH) is the most common complication of congenital heart disease(CHD). Because of the complexity and diversity of cardiac anatomy and pathophysiology, as well as a variety of adaptive mechanisms that are not fully understood, little attention is paid on pulmonary arterial hypertension associated with congenital heart disease(CHD-PAH). This article aims to summarize the clinical status, disease characteristics, outcomes, and prognosis of CHD-PAH in Pediatric Cardiology, Beijing Anzhen Hospital, proposing current unresolved issues and future challenges.