Non-compaction of ventricular myocardium in children
10.3760/cma.j.issn.2095-428X.2020.01.020
- VernacularTitle: 儿童心肌致密化不全
- Author:
Kaiyan SONG
1
;
Shu NIE
;
Yanyan HAN
Author Information
1. Department of Pediatric Cardiovascular Medicine, the First Hospital of Jinlin University, Changchun 130021, China(is working in the Department of Pediatric Cardiovascular Medicine, Qilu Children′s Hospital of Shandong University, Jinan 250022, China)
- Publication Type:Review
- Keywords:
Non-compaction of ventricular myocardium;
Cardiac insufficiency;
Arrhythmia;
Thrombosis
- From:
Chinese Journal of Applied Clinical Pediatrics
2020;35(1):70-73
- CountryChina
- Language:Chinese
-
Abstract:
Non-compaction of ventricular myocardium (NVM), a rare congenital and inherited cardiomyopathy, is characterized by prominent trabeculations and deep intertrabecular recesses in communication with the ventricular cavity.NVM has diverse clinical presentations without specificity, of which the major characteristics are cardiac insufficiency, arrhythmias and thrombosis.Echocardiography and cardiac magnetic resonance imaging are necessary technologies to diagnose NVM.Symptomatic therapy is the only choice for most patients.Furthermore, if medical treatment fails, the heart transplantation could be performed.As a whole, NVM has a high mortality and entirely different prognosis, however, the prognosis of asymptomatic patients is relatively good.
