Three-dimensional imaging of progressive facial hemiatrophy (Parry-Romberg syndrome) with unusual conjunctival findings.
10.5624/isd.2011.41.4.183
- Author:
Preethi BALAN
1
;
Subhas Babu GOGINENI
;
Shishir Ram SHETTY
;
Deepa D'SOUZA
Author Information
1. Department of Oral Medicine and Radiology, AB Shetty Memorial Institute of Dental Sciences, Nitte University, Mangalore, India. p_preethidr@rediffmail.com
- Publication Type:Case Report
- Keywords:
Facial Hemiatrophy;
Parry-Romberg Syndrome;
Pigmentation;
Conjunctiva
- MeSH:
Atrophy;
Conjunctiva;
Diagnosis, Differential;
Enophthalmos;
Facial Hemiatrophy;
Imaging, Three-Dimensional;
Pigmentation
- From:Imaging Science in Dentistry
2011;41(4):183-187
- CountryRepublic of Korea
- Language:English
-
Abstract:
Progressive hemifacial atrophy, also known as Parry-Romberg syndrome, is an uncommon degenerative condition which is poorly defined. It is characterized by a slow and progressive atrophy affecting one side of the face. The onset usually occurs during the first two decades of life. Characteristically, the atrophy progresses slowly for several years, and then it becomes stable. Ophthalmic involvement is common, with progressive enophthalmos which is a frequent finding. Cutaneous pigmentation is common in such conditions, however its extension to the conjunctiva is rarely reported. We report a case of Parry Romberg syndrome with characteristic clinical and radiographic presentation accompanied with rare ocular findings. The clinical features, radiological findings, and differential diagnoses to be considered, and the available treatment options are discussed in this report.
