A case of ectopic adrenocorticotropic hormone syndrome caused by paraganglioma mimic dermatomyositis
10.3760/cma.j.issn.1007-7480.2019.10.004
- VernacularTitle: 临床病例评析——酷似皮肌炎的副神经节瘤致异位促肾上腺皮质激素综合征一例
- Author:
Da CHEN
1
,
2
;
Hua YE
1
;
Lingli ZHOU
3
;
Songyuan GAO
4
;
Jinsong JIA
5
;
Yan XU
6
;
Yanying LIU
1
Author Information
1. Department of Rheumatology & Immunology, Peking University People's Hospital, Beijing 100044, China
2. Department of Endocrinology, Peking University People's Hospital, Beijing 100044, China
3. Department of Endocrinology, Peking University People's Hospital, Beijing 100044, China
4. Department of Pathology, Peking University People's Hospital, Beijing 100044, China
5. Department of Hematology, Peking University People's Hospital, Beijing 100044, China
6. Department of Neurology, Peking University People's Hospital, Beijing 100044, China
- Publication Type:Clinical Trail
- Keywords:
ACTH syndrome, ectopic;
Paraganglioma
- From:
Chinese Journal of Rheumatology
2019;23(10):662-665,c10-1
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To improve the recognition of ectopic adrenocorticotropic hormone syndrome.
Methods:The diagnosis and treatment of a 43 years old female patient with multiorgan involvement mimic dermatomyositis was analyzed and discussed.
Results:The patient presented with fatigue, edema, skin pigmentation, neuropsychiatric abnormalities, hypertension, hypokalemia, hyperglycemia and other systemic involvement, was finally diagnosed with ectopic adrenocorticotropic hormone syndrome caused by paraganglioma of the anterior mediastinum. After surgical removal of the tumor, her clinical symptoms immediately relieved, meanwhile related hormone levels returned to normal.
Conclusion:Although paraganglioma-induced ectopic adrenocorticotropic hormone syndrome is rare in clinical practice, more attention should be paid to this specific situation.
