A Case of Currarino Triad.
- Author:
Seung Mo PARK
;
Duk Hi KIM
;
Ho Seong KIM
- Publication Type:Case Report
- MeSH:
Constipation;
Constriction, Pathologic;
Embryonic Development;
Endoderm;
Female;
Humans;
Infant;
Neural Plate;
Notochord;
Pregnancy;
Teratoma
- From:Journal of the Korean Pediatric Society
1994;37(8):1169-1174
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Currarino triadis a unique malformation complex of congenital caudal anormalies, including anorectal malformatio (anal stenosis, anal ectopis, imperforated anus), sacral bony abnormality (scimitar or crescentic bony defect, malsegmentation) and presacral mass (meningocele, teratoma, enteric cyst or any combination of these). This triad is familial in at least half of cases and the usual symptomatology is constipation due to anorectal stenosis. The embryogenesis is presumably due to abnormal separation of the neuroectoderm from the endoderm, so this triad is in the spectrum of the split notochord syndrome. We report a case of Currarino triad in 5-month-old female patient who had chronic constipation and abdominal distention with brief review of the related literatures.
