Posterior Reversible Encephalopathy Syndrome Accompanied by a Cerebral Hemorrhage and Restricted Diffusion in a Child with Uncontrolled Nephrotic Syndrome.
10.26815/jkcns.2017.25.3.174
- Author:
Seung Mi JUNG
1
;
Seong Eun CHOI
;
Hye Jeong KIM
;
Yo Han AHN
;
Kon Hee LEE
Author Information
1. Department of Pediatrics, Hallym University Kangnam Sacred Heart Hospital, Seoul, Korea. pedlee@hallym.or.kr
- Publication Type:Case Report
- Keywords:
Posterior reversible encephalopathy syndrome;
Nephrotic syndrome;
Cerebral hemorrhage;
Diffusion magnetic resonance imaging
- MeSH:
Cerebral Hemorrhage*;
Cerebrum;
Child*;
Diffusion Magnetic Resonance Imaging;
Diffusion*;
Edema;
Female;
Follow-Up Studies;
Headache;
Humans;
Hypertension;
Magnetic Resonance Imaging;
Nephrotic Syndrome*;
Neurologic Manifestations;
Posterior Leukoencephalopathy Syndrome*;
Seizures;
Vomiting;
White Matter
- From:
Journal of the Korean Child Neurology Society
2017;25(3):174-178
- CountryRepublic of Korea
- Language:English
-
Abstract:
Posterior reversible encephalopathy syndrome (PRES) is a rare clinico-radiological syndrome that is characterized by an acute onset of headache, vomiting, visual abnormalities, confusion, and/or seizures and is typically accompanied with edema of predominantly posterior portions of the cerebral hemispheres. Here, we report a case of PRES with cerebral hemorrhage that occurred in a female pediatric patient with uncontrolled nephrotic syndrome. The patient's magnetic resonance imaging (MRI) studies showed asymmetric white matter abnormalities, cerebral hemorrhage, and restricted diffusion. After controlling her hypertension and nephrotic syndrome, her neurologic symptoms improved, and follow-up MRI findings revealed interval resolving of the white matter lesions.