Extra-adrenal pheochromocytoma after operation of congenital heart disease: a case report of 18-year-old boy.
10.4174/jkss.2012.83.1.65
- Author:
Bo Hyun HWANG
1
;
Hyun Young KIM
;
Sung Eun JUNG
;
Kwi Won PARK
Author Information
1. Department of Surgery, Seoul National University Hospital, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Pheochromocytoma;
Paraganglioma;
Fontan procedure;
Congenital heart defect
- MeSH:
Adolescent;
Blood Pressure;
Cyanosis;
Dyspnea;
Emergencies;
Follow-Up Studies;
Fontan Procedure;
Heart;
Heart Defects, Congenital;
Heart Diseases;
Hospitalization;
Humans;
Hypertension;
Outpatients;
Paraganglioma;
Pheochromocytoma;
Porphyrins;
Thoracic Surgery
- From:Journal of the Korean Surgical Society
2012;83(1):65-68
- CountryRepublic of Korea
- Language:English
-
Abstract:
Extra-adrenal pheochromocytoma is rare and presents variable symptoms. Its difficulty to diagnosis delays appropriate treatment. We would like to report an unusual case of extra-adrenal pheochromocytoma. The patient came to the emergency room with dyspnea, palpitation, and cyanosis. He had a history of hospitalization for Fontan operation due to congenital heart disease. Despite medication, his blood pressure remained high. After additional laboratory and image exams, he was diagnosed with extra-adrenal pheochromocytoma and had surgical treatment. The final pathology report was extra-adrenal pheochromocytoma with high risk of malignancy. The postoperative course was uneventful and showed normal laboratory results even after 3 months of outpatient follow-up. Extra-adrenal pheochromocytoma presents variable symptoms. We should consider endocrinologic diseases like extra-adrenal pheochromocytoma in cases presenting with palpitation and high blood pressure, even with a past history of cardiac surgery.
