Atypical Sturge-Weber Syndrome Presenting with Stroke-Like Episode
- Author:
Kyung Jin KIM
1
;
Meyung Kug KIM
;
Bong Goo YOO
Author Information
1. Department of Neurology, Kosin University College of Medicine, Busan, Korea. munguss@naver.com
- Publication Type:Case Report
- Keywords:
Sturge-Weber syndrome;
Seizure;
Stroke
- MeSH:
Aphasia;
Atrophy;
Brain;
Diffusion;
Epilepsy;
Hemangioma;
Neurocutaneous Syndromes;
Nevus;
Paresis;
Physical Examination;
Seizures;
Skin;
Stroke;
Sturge-Weber Syndrome
- From:Journal of Korean Epilepsy Society
2012;16(2):74-76
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Sturge-Weber syndrome (SWS) is a rare sporadic neurocutaneous syndrome, characterized by port-wine nevus of face, ocular vascular abnormalities and leptomeningeal angioma. A 63-year-old man developed sudden onset of right hemiparesis and global aphasia. He had a past history of epilepsy. Physical examination showed no skin lesions. Brain CT demonstrated gyriform calcification in the left frontal area. Brain MRI revealed cortical atrophy in the left hemisphere with no diffusion restrictions. Fourteen hours later, he was completely recovered from aphasia and motor weakness. We report a case of atypical SWS with episode of acute hemiparesis which highlight the difficulty in distinguishing seizure from ischemic symptoms.
