Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report
10.5933/JKAPD.2019.46.4.416
- Author:
Cheolhyeon BAE
1
;
Daewoo LEE
;
Jaegon KIM
;
Yeonmi YANG
Author Information
1. Department of Pediatric Dentistry, Jeonbuk National University Dental Hospital, Korea. pedo1997@jbnu.ac.kr
- Publication Type:Case Report
- Keywords:
CIPA;
Pain insensitivity;
Anhidrosis;
Self-mutilation
- MeSH:
Body Temperature;
Dentists;
Diagnosis;
Diagnosis, Oral;
Follow-Up Studies;
Hereditary Sensory and Autonomic Neuropathies;
Humans;
Hyperesthesia;
Hypohidrosis;
Intellectual Disability;
Pain Insensitivity, Congenital;
Reflex;
Sweat
- From:
Journal of Korean Academy of Pediatric Dentistry
2019;46(4):416-421
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disorder; affected patients are characterized by inability to feel pain and to sweat over the entire body, as well as by mental retardation. Because, in the oral examination, no specific findings on soft or hard tissue may be found except possible lesions due to self-mutilation, early recognition and diagnosis are essential for these patients. Pediatric dentists must be aware of the clinical manifestations and treatment considerations related to uncontrolled body temperature, tactile hyperesthesia and lack of pain reflex. In this case report, dental management of CIPA was suggested by presenting a 6-year follow-up of young patient.
