A case of cardiac malignant fibrous histiocytoma treated by cardiac autotransplantation.
- Author:
Hye Won JANG
1
;
Hyo Song KIM
;
Hyo Kyung CHOI
;
A Reum HAN
;
Kay Hyun PARK
;
Geung Hwan AHN
;
Joon Oh PARK
Author Information
1. Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. oncopark@smc.samsung.com
- Publication Type:Case Report
- Keywords:
Malignant fibrous histiocytoma;
Heart neoplasm;
Autologous transplantation
- MeSH:
Autografts*;
Chemotherapy, Adjuvant;
Dyspnea;
Female;
Heart;
Heart Neoplasms;
Histiocytoma, Malignant Fibrous*;
Humans;
Korea;
Middle Aged;
Sarcoma;
Transplantation, Autologous
- From:Korean Journal of Medicine
2007;73(2):223-227
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary cardiac tumors are rare findings and they are mostly benign. Malignant primary cardiac tumors make up 25% of the primary cardiac tumors and most of them are sarcomas. Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in late adulthood, and it is an extremely rare sub-type of cardiac sarcoma. It is known that MFH displays a poor clinical course with complete resection being the most important prognostic factor for survival. We described here the case of a malignant fibrous histiocytoma of the heart in a 54-year-old woman who presented with dyspnea. The tumor was treated by mass excision via cardiac explantation and autotransplantation followed by adjuvant chemotherapy. This is the first report of cardiac autotransplantation in Korea.
