MRI Finding of Retroperitoneal Desmoplastic Small Round Cell Tumor with Hepatic Metastasis and Portal Vein Thrombosis: a Case Report
10.13104/imri.2019.23.4.361
- Author:
Youe Ree KIM
1
;
Young Hwan LEE
;
Keum Ha CHOI
Author Information
1. Department of Radiology, Wonkwang University College of Medicine and Hospital, Iksan, Korea. yjyh@wku.ac.kr
- Publication Type:Case Report
- Keywords:
Desmoplastic small round cell tumor;
Retroperitoneum;
Metastasis
- MeSH:
Aged;
Desmoplastic Small Round Cell Tumor;
Female;
Humans;
Magnetic Resonance Imaging;
Male;
Mesentery;
Neoplasm Metastasis;
Omentum;
Peritoneal Cavity;
Portal Vein;
Venous Thrombosis
- From:Investigative Magnetic Resonance Imaging
2019;23(4):361-366
- CountryRepublic of Korea
- Language:English
-
Abstract:
Desmoplastic small round cell tumor (DSRCT) is a rare and aggressive malignancy common in young male patient. Typical imaging features of DSRCT include multiple soft tissue masses in the peritoneal cavity, omentum, or mesentery without an organ of origin. This report presents a rare manifestation of DSRCT revealing a solitary large retroperitoneal mass with hepatic metastasis and malignant portal vein thrombosis in 70-year-old women together with the review of literature. The tumor showed a hemorrhagic and necrotic mass with peripheral portion of T2 hypo-intensity and delayed enhancement that indicated desmoplastic stroma with dense cellularity.
