Recurrent Acute Myocardial Infarctions and Budd-Chiari Syndrome in Young Woman with Behcet's Disease.
10.4078/jkra.2007.14.1.96
- Author:
Myung Hee CHANG
1
;
So Young BANG
;
Tae Hwan KIM
;
Jae Bum JUN
;
Dae Hyun YOO
;
Sang Cheol BAE
;
Wan Sik UHM
Author Information
1. Department of Internal Medicine, The Hospital for Rheumatic Diseases, Hanyang University College of Medicine, Seoul, Korea. wsuhm@hanyang.ac.kr
- Publication Type:Case Report
- Keywords:
Behcet's disease;
Acute myocardial infarction;
Budd-Chiari syndrome
- MeSH:
Abdominal Pain;
Adult;
Aneurysm;
Anterior Wall Myocardial Infarction;
Arteries;
Arthralgia;
Budd-Chiari Syndrome*;
Cardiac Catheterization;
Cardiac Catheters;
Chest Pain;
Constriction, Pathologic;
Coronary Vessels;
Diagnosis;
Electrocardiography;
Female;
Heart Diseases;
Hepatic Veins;
Humans;
Mesenteric Artery, Inferior;
Mesenteric Artery, Superior;
Myocardial Infarction*;
Needles;
Oral Ulcer;
Prognosis;
Punctures;
Stents;
Tomography, X-Ray Computed;
Ulcer;
Vena Cava, Inferior
- From:The Journal of the Korean Rheumatism Association
2007;14(1):96-100
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We report here a case of vascular Behcet's disease. 32-year-old young woman who suffered from chest pain was diagnosed with acute myocardial infarction four years before admission. At that time she manifested symtoms of Behcet's disease, such as oral ulcers, genital ulcers, multiple arthralgia, and a peculiar hyperirritability reaction to needle puncture. At this time she was admitted due to acute chest pain and intermittent abdominal pain. The diagnosis of an acute anteroseptal myocardial infarction was made on the basis of the electrocardiography findings. Cardiac catheterization revealed segmental stenosis up to 95% at the mid-left anterior descending artery without aneurysm formation at other coronary trees and there were no atherosclerotic changes. Coronary stent was inserted in the lesion. Abdominal CT showed inferior vena cava and right hepatic vein obstruction, which supports the diagnosis of Budd-Chiari syndrome. Our case demonstrated the followings which are not common to vasculo-Behcet disease; 1) initial clinicopathologic manifestations at the coronary artery, 2) abrupt total occlusion with clear cut lesion at left anterior descending artery, 3) recurrent myocardial infarctions, 4) Budd-Chiari syndrome, 5) combined superior mesenteric artery, inferior mesenteric artery and celiac trunk obstruction. Among the systemic manifestation of Behect's disease, cardiac involvement is very rare but should be considered as one of the most important features that influences the prognosis.
