Intraductal Papillary Mucinous Neoplasm Presenting as Bleeding Duodenal Mass: A Surgical Rarity
- Author:
Nornazirah Azizan
- Collective Name:Firdaus Hayati , Andee Dzulkarnaen Zakaria , Nordashima Abd Shukor
- Publication Type:Journal Article
- Keywords:
intraductal papillary mucinous neoplasm, upper gastro intestinal bleeding, fungating duodenal mass, pancreatic invasive carcinoma
- From:
The International Medical Journal Malaysia
2019;18(1):123-126
- CountryMalaysia
- Language:English
-
Abstract:
Intraductal papillary mucinous neoplasm (IPMN) is a rare pancreatic neoplasm. The presentation varies from
recurrent pancreatitis, steatorrhea and weight loss to incidental findings during imaging studies. The
recognition of IPMN is crucial in deciding for prompt surgical intervention, which is the best treatment
modality for this precancerous condition. Here, we report a case of 55-year-old man with massive upper
gastro intestinal bleeding arising from a huge fungating duodenal mass. In view of massive bleeding, a
decision for emergency Whipple's pancreaticoduodenectomy was made. Final histological diagnosis
confirmed as IPMN. To the best of our knowledge, this is the first case of IPMN presented with a huge
fungating duodenal mass causing massive UGIB requiring surgical intervention.
- Full text:180108.pdf