IgG4 related orbit disease - An unusual cause of an orbital mass
- Author:
Chidambaram Viswanath Anand
1
Author Information
- Collective Name:Chidambaram Viswanath Anand; Anita Chan Sook Yee; Garry Choy; Chen Robert
- Publication Type:Case Reports
- From: The Medical Journal of Malaysia 2018;73(6):415-417
- CountryMalaysia
- Language:English
- Abstract: IgG4-related disease is a newly described systemic autoimmune and allergic disease, characterized histologically by a fibroinflammatory response with IgG4 plasma cells. It was initially described as affecting the pancreas, but commonly involves the head and neck region as well. While a biopsy is essential for definitive diagnosis, cross sectional imaging may be the initial modality which may suggest this entity. We describe a case of pathologically proven IgG4 related disease which highlights some key radiologic features seen in this entity. Our case highlights some key radiological features of IgG4- related disease in the head and neck, with involvement of the lacrimal glands, pituitary gland and cranial nerves on CT.
- Full text:6.2018my1362.pdf
