Inherited metabolic diseases and liver transplantation.
10.3760/cma.j.issn.1007-3418.2019.03.002
- Author:
Abuduxikuer KUERBANJIANG
1
;
J S WANG
2
,
3
Author Information
1. Department of Hepatology, Children's Hospital of Fudan University, Shanghai 201102, China.
2. Department of Hepatology, Children's Hospital of Fudan University, Shanghai 201102, China
3. Department of Pediatrics, Jinshan Hospital of Fudan University, Shanghai 200433, China.
- Publication Type:Review
- Keywords:
Genetic liver disease;
Heredity;
Liver transplantation;
Perioperative management
- MeSH:
Humans;
Liver Diseases;
Liver Transplantation;
Metabolic Diseases;
Quality of Life
- From:
Chinese Journal of Hepatology
2019;27(3):166-171
- CountryChina
- Language:Chinese
-
Abstract:
Worldwide, liver transplantation for adults and children is rapidly developing with the advancement of surgical techniques, market availability of new immunosuppressant drugs, and improved post-surgical management. Previously, liver transplantation was limited to end-stage liver disease, but recently many patients with inherited metabolic diseases achieves prolong survival and better quality of life. This article reviews the latest trends in the relationship between inherited metabolic diseases and liver, characteristics of inherited metabolic liver diseases, inherited metabolic disorders that may need liver transplantation, indications for liver transplant, and the key points of perioperative management.
