A Case of Systemic Capillary Leak Syndrome in a Child.
- Author:
Taeg Young LEE
1
;
Yoo Mi CHUNG
;
Hee Gyung KANG
;
Il Soo HA
;
Hae Il CHEONG
;
Yong CHOI
Author Information
1. Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea. ilsooha@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Systemic capillary leak syndrome;
Child
- MeSH:
Adult;
Age of Onset;
Capillaries;
Capillary Leak Syndrome*;
Child*;
Female;
Humans;
Hypoalbuminemia;
Hypotension;
Multiple Myeloma;
Paraproteinemias
- From:Journal of the Korean Pediatric Society
2002;45(10):1298-1301
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Systemic capillary leak syndrome(SCLS) is a rare disorder of unknown etiology, which is characterized by recurrent attacks of hypotension, hemoconcentration, and hypoalbuminemia. Urinary or enteric loss of protein is not demonstrated. It is often associated with monoclonal gammopathy, but does not manifest multiple myeloma. Since Clarkson et al. described the first case in a 34- year-old woman, about 50 cases have been reported in the literature. However, most of the cases were of adult age, and the mean age of onset in the reported cases was 42.6 years. In literature review, we could refer only one pediatric case of SCLC by Foeldvari et al. in 1995. We report another pediatric case of SCLS.
