Popliteal pterygium syndrome: A Case Report
10.4055/jkoa.1996.31.2.352
- Author:
Kwang Jin RHEE
;
Jun Kyu LEE
;
Chan Hee PARK
;
Young Gil WOO
;
Sang Yong LEE
- Publication Type:Original Article
- Keywords:
Popliteal pterygium syndrome
- MeSH:
Achilles Tendon;
Congenital Abnormalities;
Contracture;
Female;
Follow-Up Studies;
Foot;
Heel;
Humans;
Ischium;
Knee;
Mouth;
Nails;
Orthopedics;
Pterygium;
Skin;
Toes
- From:The Journal of the Korean Orthopaedic Association
1996;31(2):352-356
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Popliteal pterygium syndrome is rare, with 60 cases described in the literature. The syndrome includes a popliteal web extending from the ischium to the heel and other abnormalities including toenail dysplasia, deformities of the foot and toes, and oral cavity abnormalities. The main orthopedic problem is a flextion contracture of the knee and an equinus foot. We experienced a six-month-old girl with popliteal pterygium, in whom resection of abnormal fibrotic muscle belly, Achilles tendon legnthening, and Z-plastic lengthening of the skin resulted in partial correction of flexion deformity of the knee and equines contracture of the foot at one year follow-up.
