Intramedullary Nailing in Osteogenesis Imperfecta
10.4055/jkoa.1990.25.6.1624
- Author:
Kuhn Sung WHANG
;
Il Hoon SUNG
;
Sung Joon KIM
- Publication Type:Original Article
- Keywords:
Osteogenesis imperfecta;
Intramedullary nailing
- MeSH:
Classification;
Collagen;
Congenital Abnormalities;
Fracture Fixation, Intramedullary;
Humans;
Ligaments;
Lower Extremity;
Osteogenesis Imperfecta;
Osteogenesis;
Walking
- From:The Journal of the Korean Orthopaedic Association
1990;25(6):1624-1632
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Osteogenesis imperfecta is a heterogenous group of inherited disorder, which has abnormalities in the synthesis of collagen. Among variable clinical manifestations, orthopaedic clinical features are laxity of ligament and deformities arising from frequent fractures or angulation due to skeletal fragility. We had managed 4 cases of osteogensis imperfecta, which were belonged to type IV-B in two cases, type I-A in one, and type I-B in remained one by Sillence classification and they had suffered from recent fractures or deformities due to previous fractures in the long bones of the lower extremities. These patients had been treated with various types of intramedullary nails, such as Bailey-Dubow extensile rod. Rush rod and Kuntcher nail, and the result of intramedullary nailing lead to improvement of walking ability.
