Gorham's Syndrome: A Case Report
10.4055/jkoa.1990.25.4.1292
- Author:
Myung Hwan SON
;
Dong Jin KIM
;
Jae Gong PARK
;
Jang Suk CHOI
;
Young Goo LEE
- Publication Type:Case Report
- Keywords:
Gorham's syndrome;
In Korea
- MeSH:
Clavicle;
Osteoclasts;
Osteolysis;
Scapula
- From:The Journal of the Korean Orthopaedic Association
1990;25(4):1292-1296
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Gorham's syndrome is a rare disorder involing a proliferation of vascular channels associated with extensive loss of bony matrix. It starts in bone, but it may secondarily involve soft tissue and adjacent bones. Although the osteolysis usuakky arrests spontaneously, its biologic behavior is difficult to predict. The mechanism of steolysis is unkown, and the role of osteoclasts is controverwial We have experienced one case of Gorham's syndrome affecting the scapula and clavicle, which is reported in this paper with brief review of literature.
