Sjögren's Reticular Retinal Dystrophy
10.3341/jkos.2019.60.9.887
- Author:
Hoon NOH
1
;
Kunho BAE
;
Se Woong KANG
Author Information
1. Department of Ophthalmology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. kangsewoong@gmail.com
- Publication Type:Case Report
- Keywords:
Macular dystrophy;
Pattern dystrophy
- MeSH:
Choroidal Neovascularization;
Fluorescein Angiography;
Humans;
Macular Degeneration;
Male;
Middle Aged;
Retina;
Retinal Dystrophies;
Retinal Pigment Epithelium;
Retinaldehyde;
Tomography, Optical Coherence;
Vision Disorders
- From:Journal of the Korean Ophthalmological Society
2019;60(9):887-891
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: To report a rare case of Sjögren's reticular retinal dystrophy. CASE SUMMARY: A 54-year-old male presented with blurred vision and metamorphopsia in both eyes since a few years prior to his initial visit. There was a bilateral reticular network of yellow deposits throughout the posterior pole on fundus examination, which was hyperautofluorescent in fundus autofluorescence photographs. The pigment alterations were more visible with fluorescein angiography, which showed hypofluorescent lesions with hyperfluorescent borders. Spectral-domain optical coherence tomography showed elevations of the outer retina associated with the presence of subretinal hyperreflective material. Based on the conclusive correlation with clinical features, we diagnosed Sjögren's reticular retinal dystrophy. CONCLUSIONS: Sjögren's reticular retinal dystrophy is characterized by its specific pigment changes at the level of clinical manifestations and the retinal pigment epithelium. In cases of Sjögren's reticular retinal dystrophy, close monitoring is required because it has a lifetime risk of choroidal neovascularization.
