IgG4-Related Hypertrophic Pachymeningitis Mimicking Cerebral Venous Thrombosis
- Author:
Jeong Hoon BAE
1
;
Jun Sang YOO
;
Yongkyung LEE
;
Yeseul KIM
;
Su Jin SHIN
;
Hyun Young KIM
Author Information
- Publication Type:Case Report
- Keywords: IgG4-related hypertrophic pachymeningitis; Intracranial thrombosis; Histopathology
- MeSH: Fibrosis; Immunoglobulins; Intracranial Thrombosis; Meningitis; Phlebitis; Plasma Cells; Venous Thrombosis
- From:Journal of the Korean Neurological Association 2018;36(3):207-209
- CountryRepublic of Korea
- Language:Korean
- Abstract: Immunoglobulin G4-related hypertrophic pachymeningitis (IgG4-RHP) is an increasingly recognized manifestation of IgG4-related disease (IgG4-RD), which is a fibroinflammatory condition that can affect virtually any organ. The three hallmark histopathological features of IgG4-RD are lymphoplasmacytic infiltration of IgG4-positive plasma cells, storiform fibrosis, and obliterative phlebitis. We report a case of biopsy-confirmed IgG4-RHP that was initially misdiagnosed as cerebral venous thrombosis.
