Unilateral Hypoglossal Neuropathy in Multifocal Acquired Demyelinating Sensory and Motor Neuropathy: Differential Diagnosis of Motor Neuron Disease
- Author:
Sang Kyeong YOO
1
;
Min Ok KIM
;
Chang Hun KIM
;
Young Soo KIM
;
Soo Kyoung KIM
;
Heeyoung KANG
;
Nack Cheon CHOI
;
Oh Young KWON
;
Byeong Hoon LIM
;
Kee Hong PARK
Author Information
- Publication Type:Case Report
- Keywords: Peripheral demyelinating neuropathy; Motor neuron disease; Hypoglossal nerve diseases
- MeSH: Cranial Nerves; Demyelinating Diseases; Diagnosis, Differential; Humans; Hypoglossal Nerve Diseases; Incidence; Motor Neuron Disease; Motor Neurons; Peripheral Nervous System Diseases; Tongue
- From:Journal of the Korean Neurological Association 2018;36(3):210-214
- CountryRepublic of Korea
- Language:Korean
- Abstract: Multifocal acquired demyelinating sensory and motor neuropathy (MADSAM) is a peripheral neuropathy characterized by multifocal weakness and associated sensory impairment. MADSAM is associated with multifocal persistent conduction block and other signs of demyelination. The incidence of cranial nerve involvement in MADSAM was recently reported to be approximately 15%. However, reports of hypoglossal neuropathy occurring in MADSAM are rare. Unilateral hypoglossal neuropathy in MADSAM is usually misdiagnosed as motor neuron disease. We report a patient with MADSAM presenting with tongue hemiatrophy.
