Neuromyositis: A Rare Extramuscular Manifestation of Dermatomyositis
10.4078/jrd.2019.26.3.211
- Author:
Chan Keol PARK
1
;
Su Jin YOO
;
In Seol YOO
;
Jinhyun KIM
;
Seung Cheol SHIM
;
Seong Wook KANG
Author Information
1. Division of Rheumatology, Department of Internal Medicine, Chungnam National University Hospital, Daejeon, Korea. kangsw@cnuh.co.kr
- Publication Type:Case Report
- Keywords:
Dermatomyositis;
Peripheral nervous system diseases;
Nerve conduction;
Electromyography
- MeSH:
Adult;
Asia;
China;
Dermatomyositis;
Disease Progression;
Electromyography;
Europe;
Humans;
Japan;
Korea;
Lung Diseases, Interstitial;
Muscle Weakness;
Myositis;
Neural Conduction;
Peripheral Nervous System;
Peripheral Nervous System Diseases;
Polymyositis;
Skin;
United States
- From:Journal of Rheumatic Diseases
2019;26(3):211-218
- CountryRepublic of Korea
- Language:English
-
Abstract:
Dermatomyositis (DM) and polymyositis (PM) are representative idiopathic inflammatory myopathies characterized by symmetric and progressive proximal muscle weakness. Especially, DM is identified by characteristic skin lesions and has many extramuscular manifestations including various cardiac abnormalities, interstitial lung disease, and malignancy. However, involvement of peripheral nervous system in DM/PM is very rare and less known. The term “Neuromyositis” was introduced by Senator in 1893 to describe the concomitant involvement of the peripheral nervous system in DM/PM. Since then, a very few cases of neuromyositis have been reported mainly in the United States and Europe. Therefore, the pathogenetic mechanism and disease progression are unclear. In recent years, a few more cases were reported in Asia, specifically, China and Japan; however, none in Korea. Here, we describe a case of DM-associated neuromyositis in a 42-year-old man in Korea and review previous publications through literature research.
