A Case of Hepatic Inflammatory Pseudotumor Occurred in a Patient with Lupus Nephritis
10.4078/jrd.2019.26.2.137
- Author:
Min Jung KIM
1
;
Hyoungyoung KIM
;
Yeo Jin SONG
;
Soo Kyung CHO
;
Yoon Kyoung SUNG
Author Information
1. Department of Rheumatology, Hanyang University Hospital for Rheumatic Diseases, Seoul, Korea. sungyk@hanyang.ac.kr
- Publication Type:Case Report
- Keywords:
Systemic lupus erythematosus;
Liver neoplasm;
Granuloma;
Plasma cell
- MeSH:
Abdomen;
Abscess;
Adolescent;
Anti-Bacterial Agents;
Autoimmune Diseases;
Diagnosis, Differential;
Follow-Up Studies;
Granuloma;
Granuloma, Plasma Cell;
Humans;
Immunosuppressive Agents;
Liver;
Liver Neoplasms;
Lupus Erythematosus, Systemic;
Lupus Nephritis;
Magnetic Resonance Imaging;
Male;
Plasma Cells;
Prednisolone;
Rare Diseases;
Tomography, X-Ray Computed;
Ultrasonography
- From:Journal of Rheumatic Diseases
2019;26(2):137-141
- CountryRepublic of Korea
- Language:English
-
Abstract:
Systemic lupus erythematosus (SLE) is a systemic autoimmune disease affecting various organs. Among its manifestations, inflammatory pseudotumor (IPT) is an extremely rare disease about which no case has been reported of it occurring in the liver. We present a case of a SLE patient with hepatic IPT (hIPT) successfully treated with immunosuppressants. A 16-year-old male with elevated liver enzymes visited our clinic and was diagnosed as SLE. Although no lesion was observed in the initial abdomen ultrasonography, the abdominal CT on hospital day 7 revealed a new hepatic mass resembling an abscess. Despite 5 weeks of antibiotics treatment, the hepatic mass remained, and was re-diagnosed as hIPT secondary to SLE with an abdominal MRI. After high dose prednisolone and mycophenolate mofetil treatment, lupus activity subsided and hIPT disappeared in the follow-up CT. This case suggests that hIPT should be considered as a differential diagnosis among hepatic mass in SLE patients.
