Autoimmune Inner Ear Disease Mimicking Bilateral Ménière's Disease: A Case Report
10.21790/rvs.2018.17.1.28
- Author:
Hong Ju KIM
1
;
Yoon Gi CHOI
;
Hyun Ji KIM
;
Kyu Sung KIM
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, Inha University College of Medicine, Incheon, Korea. stedman@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Autoimmune inner ear disease;
Systemic lupus erythematous;
Sensorineural hearing loss
- MeSH:
Diagnosis;
Dizziness;
Ear, Inner;
Female;
Hearing;
Hearing Loss;
Hearing Loss, Sensorineural;
Hearing Loss, Sudden;
Humans;
Labyrinth Diseases;
Meniere Disease;
Middle Aged;
Rare Diseases;
Steroids;
Vertigo
- From:Journal of the Korean Balance Society
2018;17(1):28-35
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Autoimmune inner ear disease (AIED) is a rare disease, accounting for < 1% of all cases of hearing impairment or dizziness. It is characterized by sensorineural hearing loss (SNHL) or vestibular dysfunction that results from an immunemediated process. Clinical features of AIED is SNHL that progresses over weeks to month with fluctuating hearing symptoms. Because there are no diagnostic laboratory and clinical feature, response to immunosuppressive therapy were important for diagnosis of AIED. Many diseases such as sudden SNHL and Meniere disease may also mimic AIED, a broad differential must be maintained in patients suspected of having AIED. We report a case of a 46-year-old female who presented with sudden hearing loss and vertigo. We could diagnose her as AIED with systemic lupus erythematous. The symptoms were improved treated with steroids.
