A Case of Creutzfeldt-Jakob Disease Presenting Mainly with Abnormal Eye Movements
- Author:
Yeo Jeong KANG
1
;
Jun Hyun KIM
;
Tae Eun KIM
;
Sun Ah PARK
;
Tae Kyeong LEE
Author Information
1. Department of Neurology, Soonchunhyang University Bucheon Hospital, Soonchunhyang University College of Medicine, Bucheon, Korea. xorudoc@schmc.ac.kr
- Publication Type:Original Article
- Keywords:
Creutzfeldt-Jakob syndrome;
Fixation, ocular;
Nystagmus, pathologic
- MeSH:
Cerebellar Diseases;
Creutzfeldt-Jakob Syndrome;
Eye Movements;
Fixation, Ocular;
Humans;
Middle Aged;
Myoclonus;
Nystagmus, Pathologic;
Prion Diseases
- From:Journal of the Korean Balance Society
2014;13(2):53-56
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Creutzfeldt-Jakob disease (CJD) is a human prion disease with rapidly progressive neurodegeneration. The major clinical manifestations of CJD include mental deterioration, myoclonus, cerebellar dysfunction, and neuro-ophthalmic symptoms and signs. However, abnormal eye movements as an early sign of CJD are rare. We report a 49-year-old man with periodic alternating nystagmus in early disease course.