A rare case of gastric-type mucinous adenocarcinoma in a woman with Peutz-Jeghers syndrome
10.5468/ogs.2019.62.6.474
- Author:
Yeorae KIM
1
;
Eun Yi KIM
;
Tae Jin KIM
;
Kyung Taek LIM
;
Ki Heon LEE
;
Yikyeong CHUN
;
Kyeong A SO
Author Information
1. Department of Obstetrics and Gynecology, Cheil General Hospital & Women's Healthcare Center, College of Medicine, Dankook University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Adenocarcinoma;
Uterine cervical neoplasms;
Peutz-Jeghers syndrome
- MeSH:
Adenocarcinoma;
Adenocarcinoma, Mucinous;
Adenoma;
Biopsy;
Carcinoma, Squamous Cell;
Cervix Uteri;
Female;
Gastrointestinal Tract;
Humans;
Incidence;
Mucins;
Peutz-Jeghers Syndrome;
Pigmentation;
Polyps;
Uterine Cervical Neoplasms
- From:Obstetrics & Gynecology Science
2019;62(6):474-477
- CountryRepublic of Korea
- Language:English
-
Abstract:
Adenocarcinoma of the cervix is less common than squamous cell carcinoma. Minimal deviation adenocarcinoma (adenoma malignum) is considered an extremely well-differentiated variant of GAS. An association exists between GAS and Peutz-Jeghers syndrome, which is a rare autosomal dominant disorder characterized by mucocutaneous pigmentation and multiple hamartomatous polyps in the gastrointestinal tracts. The incidence of GAS in patients with Peutz-Jeghers syndrome is estimated to be 11–17%. We present a rare case of adenoma malignum, diagnosed using colposcopic biopsy in a woman with Peutz-Jeghers syndrome, which was histopathologically confirmed to be GAS after surgery.