Bilateral Renal Angiomyolipomas with Tuberous Sclerosis.
- Author:
Sang Ik KIM
1
;
Jong Hyun RYU
;
Ki Kyung KIM
Author Information
1. Kang Nam Sacred Heart Hospital, Hallym University, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
bilateral angiomyolipoma;
tuberous sclerosis;
kidney
- MeSH:
Angiofibroma;
Angiomyolipoma*;
Hemorrhage;
Intellectual Disability;
Kidney;
Retina;
Rupture, Spontaneous;
Seizures;
Tuberous Sclerosis*
- From:Korean Journal of Urology
1987;28(4):569-571
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Tuberous sclerosis is a complex neurocutaneous disease in which facial angiofibroma, mental retardation, seizures, renal tumor and phakoma of the retina are particularly frequent, in which renal tumors are usually angiomyolipomas and they are usually small, bilateral and not combined with symptom. We report a case of bilateral renal angiomyolipomas in association with facial angiofibroma, which resulted in spontaneous rupture and massive retroperitoneal hemorrhage.
