Two Cases of Recurrent Nasal Polyps in Siblings-Woakes' Syndrome
10.3342/kjorl-hns.2017.01102
- Author:
Chang Bae LEE
1
;
Nam Yoon JUNG
;
Young Jin LOH
;
Woo Yong BAE
Author Information
1. Department of Otolaryngology-Head and Neck Surgery, Dong-A University College of Medicine, Busan, Korea. doncamel@dau.ac.kr
- Publication Type:Case Report
- Keywords:
Bronchiectasis;
Endoscopic sinus surgery;
Nasal polyp;
Woakes' syndrome
- MeSH:
Bronchiectasis;
Child;
Diagnosis;
Fibrinogen;
Frontal Sinus;
Humans;
Methods;
Nasal Obstruction;
Nasal Polyps;
Plastics;
Siblings;
Young Adult
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2019;62(4):250-254
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Woakes' syndrome is a group of disease which include recurrent nasal polyps resulting in the broadening of the nasal pyramid, the onset of hypoplasia of frontal sinus and bronchiectasis, as well as the production of mucous discharge. Children and young adults are mostly susceptible to Woakes' syndrome due to the plasticity of the bone. Even though the exact etiology is unknown, genetic factor is thought to be influential because it is often diagnosed in siblings. Otolaryngologically, the mainstream method of removing nasal polyp by endoscopic sinus surgery as well as topical or systemic treatment can be helpful. We report two siblings who visited our clinic both complaining of nasal obstruction. The patients presented with recurrent nasal polyps and showed signs of bronchiectasis, which led to the diagnosis of Woakes' syndrome. These rare cases are presented here with a review of related literature.
